Hereditary angioedema: New therapeutic options for a potentially deadly disorder

BMC Hematology

Table 1 C1 inhibitor levels and complement protein concentrations in angioedemas [6].

Angioedema Type	C1 inhibitor	Functional C1 inhibitor	C4	C3	C1q
HAE type 1	<30%	<30%	Low	Normal	Normal
HAE type 2	Normal/High	<30%	Low	Normal	Normal
Inherited angioedema with normal C1 inhibitor	Normal	Normal	Normal	Normal	Normal
Acquired	Low	Low	<30%	Normal/Low	Normal/Low
Angiotensin converting enzyme inhibitor induced	Normal	Normal	Normal	Normal	Normal
Idiopathic	Normal	Normal	Normal	Normal	Normal

ISSN: 2052-1839