From: Hereditary angioedema: New therapeutic options for a potentially deadly disorder
Angioedema Type | C1 inhibitor | Functional C1 inhibitor | C4 | C3 | C1q |
---|---|---|---|---|---|
HAE type 1 | <30% | <30% | Low | Normal | Normal |
HAE type 2 | Normal/High | <30% | Low | Normal | Normal |
Inherited angioedema with normal C1 inhibitor | Normal | Normal | Normal | Normal | Normal |
Acquired | Low | Low | <30% | Normal/Low | Normal/Low |
Angiotensin converting enzyme inhibitor induced | Normal | Normal | Normal | Normal | Normal |
Idiopathic | Normal | Normal | Normal | Normal | Normal |