AS (n = 25) | SS (n = 59) | S/βThal (n = 33) | Controls (n = 118) | |
---|---|---|---|---|
Sex, F/M | 11/14 | 29/30 | 15/18 | 41/77 |
Age, years | 21.2 ± 9.1 | 16 ± 9.9 | 15.1 ± 5.1 | 20.6 ± 5.5 |
Hematological data | ||||
Hb (mg/dL) | 12.9 ± 1.67 | 8.4 ± 1.09 | 8.32 ± 1.33 | 14.1 ± 1.58 |
MCV (fL) | 81.4 ± 7.39 | 87.4 ± 8.0 | 69.16 ± 7.91 | 85.2 ± 4.08 |
MCH (pg) | 26.78 ± 2.91 | 28.7 ± 2.88 | 23.34 ± 3.41 | 31.1 ± 2.76 |
HbF (%) | 1.1 ± 0.63 | 5.14 ± 3.3 | 7.98 ± 3.43 | 0.9 ± 0.23 |
HbS (%) | 36.3 ± 6.1 | 86.6 ± 7.4 | 69.8 ± 10.56 | 0 |
Hb A2 (%) | 2.61 ± 0.41 | 2.1 ± 0.52 | 4.46 ± 0.74 | 2.4 ± 0.52 |
Clinical complications | ||||
DVT | 0 | 0 | 3 | 0 |
Stroke | 0 | 3 | 1 | 0 |
Priapism | 0 | 2 | 0 | 0 |
Leg ulcers | 0 | 9 | 0 | 0 |
AVN | 0 | 5 | 2 | 0 |