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Table 1 Characterization of SCD patients followed by the Reference Center in the South of Bahia, Brazil

From: Comparative study of sickle cell anemia and hemoglobin SC disease: clinical characterization, laboratory biomarkers and genetic profiles

Age (years) N (%) Sex N (%) Ethnicity N (%) Region of Origin N (%)
≤ 5 36 (18.0) Female 104 (52.0) Caucasian 13 (6.5) South Coast 156 (78.0)
6 to 10 44 (22.0) Male 96 (48.0) African 178 (89.0) Extreme South 29 (14.5)
11 to 15 37 (18.5)    Asian 9 (4.5) Southwest 15 (7.5)
16 to 20 21 (10.5)       
21 to 30 40 (20.0)       
≥ 31 22 (11.0)       
Number of siblings with SCD N (%) Age at 1st Diagnosis N (%) Relatives with SCD N (%) Education (by age group) N (%)
0 21 (10.5) ≤ 6 months 76 (38.0) None 100 (50.0) ≤ 5 Uneducated or incomplete 36 (18.0)
1 47 (23.5) 7 months to 4 years 50 (25.0) Father 4 (2.0)   elementary school  
2 42 (21.0) 5 to 9 years 34 (17.0) Mother 3 (1.5) 6 to 10 Uneducated or incomplete 34 (17.0)
3 33 (16.5) 10 to 14 years 11 (5.5) Brother 63 (31.5)   elementary school  
4 or More 57 (28.5) 15 to 17 years 15 (7.5) Cousin 22 (11.0)   Elementary school 10 (5.0)
   ≥ 17 years 14 (7.0) Aunt and Uncle 1 (0.5) 11 to 15 Uneducated or incomplete 24 (12.0)
     Nephews 2 (1.0)   elementary school  
     Not heard 5 (2.5)   Elementary school 13 (6.5)
     Inform   ≥ 16 Uneducated or incomplete 17 (8.5)
        elementary school  
        Elementary school 25 (12.5)
        High School 40 (20.0)
        University 1 (0.5)