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Table 1 Characterization of patients with HA who were positive for inhibitors

From: The IL-10 polarized cytokine pattern in innate and adaptive immunity cells contribute to the development of FVIII inhibitors

Patient number

Age (years)

Level of circulating FVIII

Severity

Historical peak of Bethesda titer (UB/mL)

Bethesda titer (UB/mL) at the time of blood collection

1

11

2.0

Moderate

16.0

16.0

2

19

<1.0

Severe

3.2

0.0

3

35

<1.0

Severe

384.0

20.8

4

11

2.7

Moderate

12.8

8.4

5

14

<1.0

Severe

192.0

20.8

6

13

1.9

Moderate

5.8

5.8

7

40

<1.0

Severe

93.0

16.0

8

19

<1.0

Severe

160.0

12.0

9

27

<1.0

Severe

5.4

5.4

10

6

4.0

Moderate

14.4

6.4

11

37

1.8

Moderate

128.0

0.6

12

22

<1.0

Severe

288.0

115.2

13

31

<1,0

Severe

25.6

14.4

14

14

2.9

Moderate

36.0

5,2

15

8

1.0

Severe

384.0

4.6

16

16

<1.0

Severe

7.0

2.8

17

38

<1.0

Severe

48.0

0.3

18

8

2.8

Moderate

768.0

2.0

19

10

1.0

Severe

48.0

1.2

20

36

1.5

Moderate

13.0

0.0

21

14

<1.0

Severe

52.0

13.2

22

39

<1.0

Severe

3.9

0.0

23

1

1.6

Moderate

6.6

0.5

24

23

<1.0

Severe

224.0

1.4

25

57

<1.0

Severe

20.8

1.0