From: Health related quality of life in Middle Eastern children with beta-thalassemia
Characteristic | n (%) |
---|---|
Age; median (range) | 10.0 (5 to 17) years |
Sex | |
Male | 34 (57) |
Female | 26 (43) |
Country of origin | |
Kurdistan | 10 (17) |
Libya | 8 (13) |
Palestine | 1 (2) |
Syria | 10 (17) |
Iraq | 31 (52) |
Age at diagnosis in months; median (range) | 8 (1 to 48) |
Age at first transfusion in months; median (range) | 11.5 (2 to 60) |
Age at start of iron chelation in months; median (range) | 49 (12 to 120) |
Transfusion frequency | |
Regular (pre-transfusion hemoglobin ≥ 9gr/dl) | 13 (22) |
Fairly irregular (pre-transfusion hemoglobin ≥ 7.5 and<9 gr/dl) | 34 (57) |
Irregular (Pre-transfusion hemoglobin <7.5 gr/dl or frequent transfusion reactions) | 13 (22) |
Hepatomatology > 2 cm | |
Yes | 46 (77) |
No | 13 (22) |
Unknown | 1 (2) |
Hepatitis | |
Yes | 39 (65) |
No | 21 (35) |
Ferritin >1300 ng/ml | |
Yes | 47 (78) |
No | 13 (22) |
Iron chelation | |
Regular administration (once-daily) | 13 (22) |
Slightly irregular administration (at least once a week) | 29 (48) |
Irregular administration (less than once a week or none) | 16 (27) |
None | 2 (3) |