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Table 2 Clinical and socio-demographic characteristics of 60 thalassemia children

From: Health related quality of life in Middle Eastern children with beta-thalassemia

Characteristic

n (%)

Age; median (range)

10.0 (5 to 17) years

Sex

 

 Male

34 (57)

 Female

26 (43)

Country of origin

 

 Kurdistan

10 (17)

 Libya

8 (13)

 Palestine

1 (2)

 Syria

10 (17)

 Iraq

31 (52)

Age at diagnosis in months; median (range)

8 (1 to 48)

Age at first transfusion in months; median (range)

11.5 (2 to 60)

Age at start of iron chelation in months; median (range)

49 (12 to 120)

Transfusion frequency

 

 Regular (pre-transfusion hemoglobin ≥ 9gr/dl)

13 (22)

 Fairly irregular (pre-transfusion hemoglobin ≥ 7.5 and<9 gr/dl)

34 (57)

 Irregular (Pre-transfusion hemoglobin <7.5 gr/dl or frequent transfusion reactions)

13 (22)

Hepatomatology > 2 cm

 

 Yes

46 (77)

 No

13 (22)

 Unknown

1 (2)

Hepatitis

 

 Yes

39 (65)

 No

21 (35)

Ferritin >1300 ng/ml

 

 Yes

47 (78)

 No

13 (22)

Iron chelation

 

 Regular administration (once-daily)

13 (22)

 Slightly irregular administration (at least once a week)

29 (48)

 Irregular administration (less than once a week or none)

16 (27)

 None

2 (3)