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Table 1 Hematological features of various hemoglobin E phenotypes (n = 41)

From: Hemoglobin E syndromes in Pakistani population

Phenotype

n

Hb (g/dl)

MCV (fl)

MCH (pg)

HbA (%)

HbE + A2 (%)

Hb (F %)

Others (%)

EE

6

8.8 ± 1.6

56.9 ± 4.1

17.4 ± 1.8

0

81.7 ± 1.9

2.4 ± 3.3

-

EA

20

9.7 ± 2.6

67.3 ± 8.1

21.9 ± 3.1

72.3 ± 4.3

25.9 ± 4.3

2.1 ± 3.4

-

E/β-thalassaemia

14

5.0 ± 1.8

68.1 ± 9.3

21.0 ± 3.3

19.9 ± 16.0

43.7 ± 16.3

36.3 ± 13.8

-

E/S

1

7.6

67.6

20.4

0

11.8

19.3

HbS = 68.9

All cases

41

7.9 ± 3.0

66.0 ± 8.7

20.9 ± 3.3

42.1 ± 32.1

39.8 ± 21.9

14.2 ± 18.3