Case | Sex | DC Triad | Age at Pulmonary Symptoms | Reported Pulmonary Findings | Lung Pathology (Biopsy or Autopsy) | Age Alive | Age Died | References |
---|---|---|---|---|---|---|---|---|
1 | M | 3 | 27 | CXR mottled infiltration | Fibrocystic lung dysplasia | Â | 27 | [29] |
2 | M | 2 | 23 | Respiratory illnesses | Chronic pneumonitis | Â | 31 | [30] |
3 | M | 3 | 15 | CXR diffuse coarse parenchymal infiltration | Lung segmental fibrosis | Â | 17 | [31] |
4 | M | 3 | 11 | CXR bilateral hilar enlargement and peripheral markings, bronchopneumonia | Â | Â | 11 | [32] |
5 | M | 2 | 12 | Interstitial pneumonitis, restrictive lung disease, reduced DLCO | Bronchiocentric granulomatosis, obliteration of respiratory passages | 12 | Â | [33] |
6 | F | 3 | 20 | Diffuse interstitial pneumonitis, hypoxia, restrictive airway disease | Obliteration of bronchiolar lamina, mild interstitial pneumonitis | Â | 20 | [33] |
7 | M | 3 | 39 | Mild restrictive impairment, CXR coarse reticular pattern | Pneumothorax, nonspecific collagenous interstitial fibrosis | Â | 39 | [34] |
8 | M | 2 | 46 | Restrictive impairment, reduced diffusion. CT patchy high density areas and ring-like opacities | Focal fibrosis; UIP | 46 | Â | [35] |
9 | M | 3 | 10 | Restrictive pulmonary function, CT interstitial thickening and honeycombing | Fibrosis, reticular fibers. | Â | 10 | |
10 | M | 3 | 30 | CT Interstitial lung fibrosis, DLCO 44% | Focal interstitial fibrosis, UIP | 38 | Â | |
11 | M | 2 | 51 | CXR ground glass opacities | Organizing diffuse alveolar damage, UIP | Â | 51 | [40] |
12 | M | 3 | 40 | Restrictive function, CT ground glass, honeycombing | Fibrosis, UIP | Â | 43 | [41] |
13 | F | 3 | 32 | Interstitial fibrosis | Â | Â | 32.9 | [42] |
14 | M | 3 | 48 | Restrictive pattern, DLCO 30%, CT UIP | Â | Â | 48 | [43] |
15 | F | 3 | 40 | Surgery, XRT, chemotherapy for pharynx SCC at age 28; respiratory insufficiency age 40 | Â | 40 | Â | [44] |
16 | M | 3 | 37 | Pulmonary function, and CT, pulmonary fibrosis | Â | Â | 37.7 | [45] |
17 | M | 2 | 41 | Pulmonary fibrosis | Â | 41 | Â | [46] |
18 | M | 3 | 37 | Bronchitis | Â | 37 | Â | [46] |
19 | F | 3 | 30 | Interstitial fibrosis age 31 yr, left pneumothorax, then right pneumothorax | Â | Â | 32 | [47] |
20 | F | 2 | 12 | Interstitial pneumonitis | Â | 12 | Â | [5] |
21 | F | 1 | 52 | Pulmonary fibrosis | Â | 52 | Â | [5] |
22 | M | 1 | 68 | Pulmonary fibrosis | Â | Â | 68 | |
23 | M | 1 | 45 | Pulmonary fibrosis | Â | Â | 47 | |
24 | F | 0 | 63 | Pulmonary fibrosis | Â | Â | 65 | [19] |
25 | M | 0 | 52 | Pulmonary fibrosis | Â | 52 | Â | [19] |
26 | F | 0 | 54 | Pulmonary fibrosis | Â | 54 | Â | [19] |
27 | M | 0 | 21 | Pulmonary fibrosis | Â | 22 | Â | [19] |
28 | F | 0 | 64 | Fibrosing alveolitis | Â | Â | 64 | [20] |
29 | M | 0 | 60 | Cryptogenic fibrosing alveolitis, heart/lung transplant | Â | 60 | Â | [20] |
30 | M | 0 | 35 | Pulmonary symptoms | Â | Â | 35 | [21] |
31 | M | 0 | 24 | Pulmonary symptoms | Â | Â | 24 | [21] |
32 | M | 0 | 7 | Restrictive interstitial pulmonary disease | Â | Â | 7 | [21] |
33 | M | 0 | 33 | CT lungs fibrotic changes both apical regions | Â | 33 | Â | [21] |
34 | F | 0 | 44 | Restrictive pattern, decreased diffusion, CT pulmonary fibrosis | Â | Â | 46 | [22] |
35 | M | 0 | 32 | Â | Diffuse interstitial pulmonary fibrosis | Â | 32 | [22] |
36 | M | 0 | 50 | Decreased diffusion, CT pulmonary fibrosis | Â | Â | 50 | [22] |
37 | F | 0 | 37 | Pulmonary fibrosis | Â | Â | 37 | [22] |